Volume 5, Issue 6, November 2019, Page: 76-79
A Rare Case of Gerbode Defect and Review of Literature
Anirudh Kumar Paidi, Department of Cardiovascular and Thoracic Surgery, Yashoda Hospitals, Hyderabad, India
Palli Venkata Naresh Kumar, Department of Cardiovascular and Thoracic Surgery, Yashoda Hospitals, Hyderabad, India
Ravikanth Vanguri, Department of Cardiac Anaesthesia, Yashoda Hospitals, Hyderabad, India
Rajasekhar Varada, Department of Cardiology, Yashoda Hospitals, Hyderabad, India
Madhav Rao Midhe, Department of Cardiac Anaesthesia, Yashoda Hospitals, Hyderabad, India
Ravi Kiran Mamidala, Department of Cardiovascular and Thoracic Surgery, Yashoda Hospitals, Hyderabad, India
Received: Oct. 26, 2019;       Accepted: Nov. 19, 2019;       Published: Nov. 25, 2019
DOI: 10.11648/j.ijcts.20190506.11      View  79      Downloads  35
Abstract
A Gerbode defect is a very rare type of congenital anomaly with a direct communication between left ventricle and right atrium leading to Left to Right shunt. This defect was first reported by Meyer in 1857. First successful closure was done by Kerby et al using hypothermia and inflow occlusion technique. It may present as a direct or indirect type. With improvements in nomenclature and taxonomy that expanded the classification until the current modifications were in place that accounted for defect type and position with respect to the Tricuspid Valve. Now, it is broadly described as Supravalvular type and infravalvular type. The etiology is typically congenital with irregularities emerging by perforation of anterior intraventricular septum, malformation of leaflets, or widening of the commissural space. These embryological deviations subsequently permit an abnormal communication that begins the physiological processes leading to the pathology. Shunt depends on the size of the defect and PVR. Shunt flow begins inutero because of the obligatory difference in the systolic pressure between LV and RA. RA accepts shunt with less or no elevation of pressures due to distensibility. We report a 8 year old female child who presented with dyspnea on exertion and recurrent respiratory infections whose echocardiography confirmed a direct type (supravalvular) Gerbode defect. This was confirmed by cath study and during surgery. She underwent successful suture closure of the shunt using a Goretex patch. This is a case of direct type Gerbode defect doing well after surgery.
Keywords
Gerbode Defect, Congenital Anomaly, Left to Right Shunt, Direct, Indirect, Ventricular Septal Defect, Tricuspid Valve
To cite this article
Anirudh Kumar Paidi, Palli Venkata Naresh Kumar, Ravikanth Vanguri, Rajasekhar Varada, Madhav Rao Midhe, Ravi Kiran Mamidala, A Rare Case of Gerbode Defect and Review of Literature, International Journal of Cardiovascular and Thoracic Surgery. Vol. 5, No. 6, 2019, pp. 76-79. doi: 10.11648/j.ijcts.20190506.11
Copyright
Copyright © 2019 Authors retain the copyright of this article.
This article is an open access article distributed under the Creative Commons Attribution License (http://creativecommons.org/licenses/by/4.0/) which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
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