Volume 5, Issue 6, November 2019, Page: 80-83
Successful Surgical Repair of Scimitar Syndrome in a 38-Year-Old Adult
Rafael Meza, Department of Congenital Heart Surgery, Somer in Care Cardiovascular Center, Rionegro, Colombia
John Araujo, Department of Pediatric and Adult Congenital Heart Disease, Somer in Care Cardiovascular Center, Rionegro, Colombia
Alejandro Escobar, Department of Congenital Heart Surgery, Somer in Care Cardiovascular Center, Rionegro, Colombia
Alejandra Echeverri, Department of Pediatric and Adult Cardiovascular Anesthesiology, Somer in Care Cardiovascular Center, Rionegro, Colombia
Juan Turizo, Department of Congenital Heart Surgery, Somer in Care Cardiovascular Center, Rionegro, Colombia
Susana Cardona, Department of Congenital Heart Surgery, Somer in Care Cardiovascular Center, Rionegro, Colombia
Received: Nov. 30, 2019;       Accepted: Dec. 19, 2019;       Published: Jan. 7, 2020
DOI: 10.11648/j.ijcts.20190506.12      View  159      Downloads  72
Abstract
Scimitar syndrome is an infrequent congenital malformation. It is a partial anomalous pulmonary venous drainage of the right lung into the inferior vena cava. Up to 25% of cases are associated with other heart diseases. The incidence in adults is reported to be 0.5-0.7%; classically, the adult form does not have pulmonary arterial hypertension, and may be unnoticed and asymptomatic for many years. It often presents after the second decade of life with nonspecific symptoms. Without surgical repair, clinical worsening, increased pulmonary pressure and sustained pulmonary arterial hypertension ultimately occur, when the syndrome is associated with other congenital heart diseases. We present the case of a 38-year-old woman diagnosed with scimitar syndrome associated with a large superior sinus venosus atrial septal defect, who underwent successful surgical repair using a lateral pericardial tunnel technique to redirect right pulmonary venous flow to the left atrium through a left atriotomy. This repair has shown good medium-term results. Possible complications such as tunnel thrombosis and stenosis will need to be explored in future assessments, and follow up must be lifelong.
Keywords
Scimitar Syndrome, Partial Anomalous Pulmonary Venous Drainage, Adult Congenital Heart Disease, Pericardial Tunnel
To cite this article
Rafael Meza, John Araujo, Alejandro Escobar, Alejandra Echeverri, Juan Turizo, Susana Cardona, Successful Surgical Repair of Scimitar Syndrome in a 38-Year-Old Adult, International Journal of Cardiovascular and Thoracic Surgery. Vol. 5, No. 6, 2019, pp. 80-83. doi: 10.11648/j.ijcts.20190506.12
Copyright
Copyright © 2019 Authors retain the copyright of this article.
This article is an open access article distributed under the Creative Commons Attribution License (http://creativecommons.org/licenses/by/4.0/) which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
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